英文名称
Beta-Hydroxyisovaleric Acid-d8
Smiles Code
OC(C([2H])([2H])[2H])(C([2H])([2H])[2H])C([2H])([2H])C(O)=O
Building Blocks; Isotopic Labeled Analogues; Pharmaceutical/API Drug Impurities/Metabolites;
b-Hydroxyisovaleric Acid-d8 is the isotope labelled analog of b-Hydroxyisovaleric Acid (H943605); a metabolite of the essential amino acid Leucine. It is synthesized in the human body and studies suggest that b-Hydroxyisovaleric Acid may have an effect on increasing muscle weight and strength. The presence of elevated b-Hydroxyisovaleric Acid is a sensitive marker of biotin deficiency and may indicate the presence of a genetic disorder such as biotinidase deficiency or holocarboxylase synthetase deficiency.